Benefits of Physical exercise in pulmonary arterial hypertension associated with uncorrected congenital heart disease
Introduction: congenital heart disease is classified as one of the main groups to develop pulmonary arterial hypertension. The exercise program can help to improve daily living, capacity, clinical and functional improvement, minimizing the deleterious consequences of the disease.
Case report: we report a case of a 31-year-old male patient with a clinical diagnosis of severe pulmonary arterial hypertension due to the right ventricular double outflow tract with interventricular communication without surgical intervention. After being referred to the Cardiopulmonary and Metabolic Rehabilitation program at a cardiology reference center in Rio Grande do Sul, clinical evaluation was performed, as well as functional capacity by the 6-minute walk test, muscle strength and peripheral resistance by the sitting-rising test, and respiratory muscle strength by the manovacuometry exam. The values were below the predicted value. The proposed exercise program was performed during 30 sessions consisting of aerobic exercises lasting 33 minutes, added strength training of large muscle groups.
Conclusion: after the program there was an increase of 83 meters in the 6-minute walk test and an increase in respiratory muscle strength, as well as a reduction in Borg scale parameters.
Brasil. Ministério da Saúde. Portaria n.º 1.727, de 11 de julho de 2017. Aprova o Plano Nacional de Assistência à Criança com Cardiopatia Congênita. Diário Oficial da República Federativa do Brasil [Online] 2017 maio [acesso 15 mar. 2020]. Disponível em: https://portalarquivos2.saude.gov.br/images/pdf/2017/julho/31/Portaria-1727.pdf
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