Dentinogenesis imperfecta in siblings: a case report

Luciana M.P.S. Ramos Fernandes, Maria Helena Hiar Rodriguez, César Ângelo Lascala


Purpose: The present article reports the diagnosis and treatment of two siblings with dentinogenesis imperfecta (DI) type II.
Case description: Two Caucasian children, thirteen and six-years old, male and female gender, respectively, had teeth with dentinogenesis imperfecta type II. The patients did not have any associated systemic disease. Dentinogenesis imperfecta is a dental development disorder, characterized by dentin defects in both primary and permanent dentitions. The affected teeth have color alteration, most often of bluish-gray or yellowish-brown color; with short and bulbous shaped crowns with dentin exposure and attrition. Radiographically, the teeth show short constricted root and pulp chamber obliteration. The thirteen-year old boy with permanent teeth received orthodontic treatment with a removable appliance and dental bleaching. The six-year old girl with mixed dentition received dentures adapted over the remaining teeth that were in good clinical conditions for maintenance.
Conclusion: It is important that the dentist knows how to diagnose the early manifestations of DI to provide professional orientation on the dental alterations and adequate care. The treatment should be conservative aiming to preserve dental substrate and reestablish function and esthetics.
Key words: Dentinogenesis imperfecta; hereditary opalescent dentin; abnormalities; Pediatric Dentistry


Dentinogenesis imperfecta; hereditary opalescent dentin; abnormalities; Pediatric Dentistry

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e-ISSN: 1980-6523

ISSN-L: 0102-9460


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